Alpha galactosidase A antibody

Volume: 100 µg Purification: Protein A+G purification Form: liquid Purity: 95% as determined by SDS-PAGE Host: Mouse Clonality: monoclonal Clone ID: 7F1 Isotype: IgG2a Storage: PBS with 0.02% sodium azide and 50% glycerol pH 7.3,-20? for 12 months(Avoid repeated freeze / thaw cycles.) Background: GLA, also named as Melibiase, Agalsidase and Alpha-galactosidase A, belongs to the glycosyl hydrolase 27 family. It hydrolyzes terminal, non-reducing alpha-D-galactose residues in alpha-D-galactosides, including galactose oligosaccharides, galactomannans and galactolipids. Fabry disease is an X-linked lysosomal storage disorder resulting from the deficient activity of GLA. Enzyme replacement therapy(ERT) with GLA is currently the most effective therapeutic strategy for patients with Fabry disease, a lysosomal storage disease. Immunogen: galactosidase, alpha Synonyms: Alpha galactosidase A, galactosidase, alpha Observed MW: 49 kDa Uniprot ID: P06280 Reactivity: Human Tested Application: ELISA, WB, IHC, IF Recommended dilution: WB: 1: 500-1: 2000; IHC: 1: 20-1: 200; IF: 1: 20-1: 200 Gene ID: 2717 Research Area: Cardiovascular, Metabolism, Signal Transduction